The absolute amount of 13C6-GlcNS-GlcUA in the vial was determined using quantitative NMR to have the stated value on the vial. The vial has additional components, but none are isobaric with 13C6-GlcNS-GlcUA, and these additional components have no effect on the ability to quantify the 13C6-GlcNS-GlcUA.

13C6-GlcNS-GlcUA (GAG Endogenous NRE)

SKU: BM12B

Quantity

Herbst, Z.M., Hong, X., Urdaneta, L., Klein, T., Waggoner, C., Liao, H.C., Kubaski, F., Giugliani, R., Fuller, M. and Gelb, M.H., 2023. Endogenous, non-reducing end glycosaminoglycan biomarkers are superior to internal disaccharide glycosaminoglycan biomarkers for newborn screening of mucopolysaccharidoses and GM1 gangliosidosis. Molecular Genetics and Metabolism, 140(1-2), p.107632. DOI: 10.1016/j.ymgme.2023.107632

13C6-GlcNS-GlcUA (GAG Endogenous NRE)

PRODUCT INFO

RELEVANT LITERATURE

SDS