IdoUA-ß(1→4)-GlcNAc6S ("IdoUA-GlcNAc6S") is the GAG Endogenous NRE (EndoNRE) quantitative standard associated with IDUA

The absolute amount of IdoUA-GlcNAc6S in the vial was determined using quantitative NMR to have the stated value on the vial. The vial has additional components, but none are isobaric with IdoUA-GlcNAc6S, and these additional components have no effect on the ability to quantify the IdoUA-GlcNAc6S.

IdoUA-GlcNAc6S (GAG EndoNRE)

SKU: BM14D

Quantity

Singh, G., Gholap, S.P., Lim, S., Herbst, Z.M. and Gelb, M.H., 2026. Synthesis of the Endogenous Non-Reducing End Heparan Sulfate Disaccharides for Newborn Screening and Diagnosis of Mucopolysaccharidosis types I and II. Carbohydrate Research, p.110100. DOI: 10.1016/j.carres.2026.110100

Herbst, Z.M., Urdaneta, L., Klein, T., Burton, B.K., Basheeruddin, K., Liao, H.C., Fuller, M. and Gelb, M.H., 2022. Evaluation of two methods for quantification of glycosaminoglycan biomarkers in newborn dried blood spots from patients with severe and attenuated mucopolysaccharidosis type II. International Journal of Neonatal Screening, 8(1), p.9. DOI: 10.3390/ijns8010009

IdoUA-GlcNAc6S (GAG EndoNRE)

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