Each kit includes:
• Vials of dried, pre-mixed substrates and internal standard (qNMR quantified) for MS/MS duplex enzyme assay of β-Hexosaminidase A (HexA) and Total β-Hexosaminidase (Total Hex).
• The relevant Enzyme Assay Buffer.
First order comes with qNMR quantified enzymatic products relevant to the HexA and Total Hex enzyme assays, for mass spectrometry tuning and standard curve generation (See Absolute Quantification).
Patent pending.
TaySachs, Tay-Sachs, Sandhoff, GM2-gangliosidosis
Duplex Assay Cocktail of β-Hexosaminidase A and Total β-Hexosaminidase
SKU: CD5
Catalog Number: CD5