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Each kit includes:

 

• Vials of dried, pre-mixed substrates and internal standards (qNMR quantified) for MS/MS 6-plex enzyme assays of α-L-Iduronidase, Acid α-glucosidase, α-Galactosidase A, Galactosylceramidase, Acid β-glucocerebrosidase and Acid sphingomyelinase.

 

• The relevant Enzyme Assay Buffer.

 

First order comes with qNMR quantified enzymatic products relevant to the IDUA, GAA, GLA, GALC, GBA and SMPD1 enzyme assays, for mass spectrometry tuning and standard curve generation (See Absolute Quantification).

 

"Minimum order quantity: 10 vials (500  6-plex assays)"

 

MPS-I ;Fabry; Pompe; Gaucher; Krabbe; Neimann Pick A/B

6-plex assay cocktail of IDUA, GAA, GLA, GALC, GBA and SMPD1 Enzymes

SKU: CM2
  • Catalog Number: CM2

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