Each kit includes:
• Vials of dried, pre-mixed substrate and internal standard (qNMR quantified) for MS/MS enzyme assay of Arylsulfatase A (ARSA).
• The gel filteration medium for size-exclusion chromatography (needed for the assay with DBS).
• The relevant Enzyme Assay Buffer.
First order comes with qNMR quantified enzymatic product relevant to the ARSA enzyme assay, for mass spectrometry tuning and standard curve generation (See Absolute Quantification).
MLD Metachromatic Leukodystrophy
Arylsulfatase A Assay Cocktail
SKU: CS12
The mixture contains: d3-C18:0-sulfatide (MW=811.2) and d7-C18:0-galactosylceramide (MW= 735.2).
Catalog Number: CS12