Each kit includes:
• Vials of dried, pre-mixed substrate and internal standard (qNMR quantified) for MS/MS enzyme assay of Acid α-glucosidase (GAA).
• The relevant Enzyme Assay Buffer.
First order comes with qNMR quantified enzymatic product relevant to the GAA enzyme assay, for mass spectrometry tuning and standard curve generation (See Absolute Quantification).
Pompe
Acid α-Glucosidase Assay Cocktail
SKU: CS5
The mixture contains t-butyl (7-benzamidoheptyl){3-[(4-hydroxyphenyl)amino]-3-oxopropyl}carbamate-α-glucoside (MW=659.77) and t-butyl (7-benzamidoheptyl){3-[(4-hydroxyphenyl)amino]-3-oxopropyl}carbamate-d5 (MW=502.66).
Catalog Number: CS5