Each kit includes:
• Vials of dried, pre-mixed substrate and internal standard (qNMR quantified) for MS/MS enzyme assay of α-Galactosidase A (GLA).
• The relevant Enzyme Assay Buffer.
First order comes with qNMR quantified enzymatic product relevant to the GLA enzyme assay, for mass spectrometry tuning and standard curve generation (See Absolute Quantification).
"Minimum order quantity: 10 vials (500 assays)"
Fabry
α-Galactosidase A Assay Cocktail
SKU: CS7
The mixture contains t-butyl (6-benzamidohexyl){3-[(4-hydroxyphenyl)amino]-3-oxopropyl}carbamate-α-galactoside (MW=645.74) and t-butyl (6-benzamidohexyl){3-[(4-hydroxyphenyl)amino]-3-oxopropyl}carbamate-d5 (MW=488.63).
Catalog Number: CS7